Wang Rui,Peng Kun,Ma Tidong,et al.Individualized surgical management and rehabilitation of perineal single-orifice cloaca in infants and young children[J].Journal of Clinical Pediatric Surgery,,():741-744.[doi:10.3760/cma.j.cn101785-202310049-007]
Individualized surgical management and rehabilitation of perineal single-orifice cloaca in infants and young children
- Keywords:
- Anorectal Malformations; Cloaca With Single Perineal Orifice; Surgical Procedures; Operative; Enterostomy; Individualized Treatment; Defecation; Urination; Treatment Outcome
- Abstract:
- Objective To summarize individualized surgical techniques,postoperative rehabilitation,and follow-up for perineal single-orifice cloaca in infants and young children,providing a reference for its diagnosis and treatment. Methods The clinical data of 5 patients with single-orifice cloaca treated at Hunan Children‘s Hospital between October 2016 and October 2023 were reviewed retrospectively.Pre-operative findings,diagnostic work-up,operative procedures,postoperative rehabilitation,and long-term follow-up were collected and analyzed. Results All 5 patients were female and first evaluated on day 1 of life.After definitive diagnosis,transverse colostomy was performed at 2-6 days of age.Cystoscopy revealed common channel (CC) lengths of 1.6 cm,2.0 cm,2.5 cm,3.0 cm,and 4.0 cm;urethral lengths of 2.3 cm,3.0 cm,3.2 cm,3.4 cm,and 4.5 cm;and vaginal lengths of 2.0 cm,2.8 cm,3.0 cm,3.1 cm,and 4.5 cm,respectively.Individualized definitive repair was carried out:posterior sagittal anorectoplasty (PSARP) plus total urogenital mobilization (TUM) in two cases,and laparoscopically assisted anorectoplasty (LAARP) plus TUM in three cases.No severe postoperative complications occurred.Voiding function scores showed two cases in Grade Ⅱ and two cases in Grade Ⅰ (one infant <2 years old was not scored).Bladder residual volume ≤ 8 mL was recorded 3 months after stoma closure in all patients.Bowel function assessment yielded scores of 6 and 5 in two evaluable children. Conclusions Individualized treatment and rehabilitation for perineal single-orifice cloaca in infants and young children achieves satisfactory clinical outcomes and is suitable for broader clinical application.
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Memo
收稿日期:2023-10-27。
基金项目:湘财社指[2024]0083号
通讯作者:王睿,Email:15189690@qq.com