Liang Mingqian,Li Haichong,Zhang Xuejun,et al.Clinical analysis of traditional growing rods technique for neurofibromatosis type 1 dystrophic scoliosis[J].Journal of Clinical Pediatric Surgery,2025,(04):320-325.[doi:10.3760/cma.j.cn101785-202410065-004]
Clinical analysis of traditional growing rods technique for neurofibromatosis type 1 dystrophic scoliosis
- Keywords:
- Neurofibromatosis Type 1; Scoliosis; Dystrophy; Traditional Growing Rods; Intraoperative Complications; Postoperative Complications; Treatment Outcome
- Abstract:
- Objective To explore the clinical efficacies and related complications of bilateral traditional growing rods (TGRs) for neurofibromatosis type 1 (NF1) dystrophic scoliosis.Methods From March 2016 to July 2021,the clinical data were retrospectively reviewed for 31 children with NF1 dystrophic scoliosis.All children were treated with TGRs and underwent re-expansion regularly.Cobb angle,T1-T12 height (TTH),T1-S1 height (TSH),trunk shift (TS),local kyphosis (LK) and sagittal vertebral axis (SVA) were measured before,after operation and at the last follow-up.Results There were 17 boys and 14 girls with an average age of initial operation 6.8 years.Immediately post-operation,Cobb angle was compared with that pre-operation ,TTH ,TSH and LK.Both TS and SVA significantly improved compared with those pre-operation (P<0.05).Follow-up period was (2-7) years.At the last follow-up,Cobb angle was (26.8±13.3)°,TTH (22.1±2.8)cm and TSH (36.1±4.0)cm.All differences were statistically significant (P<0.05).During follow-ups,there were screw displacement (n=4),growing rod fracture (n=3) and distal adding-on phenomenon (n=1).The incidence of complications was 26%.Conclusions TGRs technique is both safe and effective for children with NF1 dystrophic scoliosis.It may effectively control the progress of spinal deformities while preserving the growth capability of spine and thorax.
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Memo
收稿日期:2024-10-28。
基金项目:中央高水平医院临床科研基金(2022-PUMCH-D-004);国家重点研发计划(2023YFC2507701)
通讯作者:张学军,Email:zhang-x-j04@163.com