Qiao Qi,Zhang Zhibo.Comprehensive managements after Kasai portoenterostomy for biliary atresia[J].Journal of Clinical Pediatric Surgery,,20():133-139.[doi:10.12260/lcxewkzz.2021.02.006]
Comprehensive managements after Kasai portoenterostomy for biliary atresia
- Keywords:
- Biliary Atresia/SU; Cholangitis/CO; Surgical Procedures; Operative
- CLC:
- R657.4+4 R726.1
- Abstract:
- Biliary atresia (BA) is a disease of progressive inflammation and fibrosis of intra/extrahepatic bile ducts in infants.Its etiology and mechanism of progression have remained ill elucidated.Kasai portoenterostomy (KPE) is a first choice for biliary atresia.Successful KPE operation may reconstruct bile drainage.However,the long-term native liver survival (NLS) after KPE operation is relatively low and children often suffer from various complications.Most children require liver transplantation before adulthood.Comprehensive managements after KPE have great impact on NLS and long-term quality of life of children.And how to improve postoperative managements is vital for the prognosis of BA.
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Memo
收稿日期:2020-05-08。
基金项目:国家自然科学基金(编号:81270437);辽宁科技厅项目(编号:2017225014)
通讯作者:张志波,Email:zhangzb@sj-hospital.org