Wang Zhe,He Qiuming,Wang Haiyu,et al.Evaluation and treatment of prenatal persistent cloaca: two case reports and literature review[J].Journal of Clinical Pediatric Surgery,,19():884-890.[doi:10.3969/j.issn.1671-6353.2020.10.005]
Evaluation and treatment of prenatal persistent cloaca: two case reports and literature review
- CLC:
- R726.1;R726.2;R657.1;R714.5
- Abstract:
- Objective To review the prenatal diagnosis and treatments of 2 girls of persistent cloaca malformation and summarize the experiences of prenatal diagnosis,evaluations and neonatal treatments.Methods From January 2017 to December 2019,two girls with cloacal malformation underwent radical surgery.Their clinical characteristics were analyzed by retrieving their medical records and imaging data.The initial abnormalities of case 1 were intestinal dilation and enhanced echo of meconium.Abnormal appearance of external genitalia and minimal bilateral vaginal fluid were found during the third trimester.Cloaca malformation was diagnosed.Transverse colonostomy,radical surgery and stoma closure were performed in sequence.The prenatal abnormality of case 2 was massive hydrocolpos and left hydronephrosis accompanied by ureteral dilatation.She was diagnosed as cloaca malformation.Transverse colostomy,vaginostomy and cystostomy were performed successively postnatally and then radical surgery and stoma closure completed.Both girls had a good prognosis.Results A total of 38 papers were retrieved,including 1 in Chinese and 37 in English.Complete reports were reviewed for 13 fetuses with cloaca deformities before delivery.And hydrocolpos was the most common prenatal sign.Three fetuses required prenatal interventions due to urinary retention.And 9 fetuses survived after birth.Conclusion Although prenatal diagnosis of cloaca malformations has made great advances,there are still some difficulties.The sequential treatment of "seamless integration" between fetus and newborn shall become a new model for actively changing the treatments and prognosis of cloaca malformations.
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Memo
收稿日期:2020-03-10。
通讯作者:钟微,Email:zhongwei@gwcmc.org