Zheng Shan.Several outstanding issues in long-term survival of children with biliary atresia[J].Journal of Clinical Pediatric Surgery,,19():469-472.[doi:10.3969/j.issn.1671-6353.2020.06.001]
Several outstanding issues in long-term survival of children with biliary atresia
- Keywords:
- Biliary Atresia; Therapy; Quality of Life; Child
- CLC:
- R722;R575.7;R725.7
- Abstract:
- The diagnosis and treatment of children with biliary atresia (BA) in China mainland have significantly improved.However,long-term native liver survival rate and quality of life should be further optimized.Long-term standard follow-ups of Kasai postoperative complications and liver fibrosis,comprehensive treatments with multidisciplinary cooperations,long-term monitoring of growth and development,reasonable nutrition and vaccination guidance and appropriate timing for liver transplantation are the critical factors to help BA children to obtain long-term high-quality survival.
References:
1 Dong R,Jiang J,Zhang S,et al.Development and validation of novel diagnostic models for biliary atresia in a large cohort of chinese patients[J].E Bio Medicine,2018,34:223-230.DOI:10.1016/j.ebiom.2018.07.025.
2 余莉,黄维勇,郭勇,等.比色卡提高医生对陶土色大便识别的调查研究[J].临床小儿外科杂志,2019,18(8):692-698.DOI:10.3969/j.issn.1671-6353.2019.08.015.Yu L,Huang WY,Guo Y,et al.Evaluations of infant stool color card in detecting discolored stools by physicians[J].J Clin Ped Sur,2019,18(8):692-698.DOI:10.3969/j.issn.1671-6353.2019.08.015.
3 Yang L,Zhou Y,Xu PP,et al.Diagnostic accuracy of serum matrix metalloproteinase-7 for biliary atresia[J].Hepatology,2018,68(6):2069-2077.DOI:10.1002/hep.30234.
4 葛亮,詹江华.胆道闭锁肝纤维化与自体肝生存关系的研究进展[J].临床小儿外科杂志,2020,19(2):171-175.DOI:10.3969/j.issn.1671-6353.2020.02.016.Ge L,Zhan JH.Relationship between liver fibrosis and native liver survival in infants with biliary atresia[J].J Clin Ped Sur,2020,19(2):171-175.DOI:10.3969/j.issn.1671-6353.2020.02.016.
5 Nio M.Japanese Biliary Atresia Registry[J].Pediatr Surg Int,2017,33(12):1319-1325.DOI:10.1007/s00383-017-4160-x.
6 段星星,彭娅,刘凌萍,等.超声剪切波弹性成像技术对胆道闭锁筛查与诊断的临床价值分析[J].临床小儿外科杂志,2018,17(11):821-825.DOI:10.3969/j.issn.1671-6353.2018.11.005.Duan XX,Peng Y,Liu LP,et al.Value of shear wave elastography in differentiating biliary atresia from cholestatic hepatitis in infants[J].J Clin Ped Sur,2018,17(11):821-825.DOI:10.3969/j.issn.1671-6353.2018.11.005.
7 Peck-Radosavljevic M.Thrombocytopenia in chronic liver disease[J].Liver Int,2017,37(6):778-793.DOI:10.1111/liv.13317.
8 陈功,郑珊.《中国大陆地区胆道闭锁诊断及治疗(专家共识)》解读[J].中华小儿外科杂志,2014,35(4):311-314.DOI:10.3760/cma.j.issn.0253-3006.2014.04.017.Chen G,Zheng S.Interpretation of Expert Consensus on the Diagnosis and Treatment of Biliary Atresia in Mainland China[J].Chin J Pediatr Surg,2014,35(4):311-314.DOI:10.3760/cma.j.issn.0253-3006.2014.04.017.
9 向波,谢小龙.胆道闭锁的"Kasai手术-肝移植"序贯治疗[J].临床小儿外科杂志,2018,17(11):805-808.DOI:10.3969/j.issn.1671-6353.2018.11.002.Xiang B,Xie XL.Sequential Kasai procedure-liver transplantation for biliary atresia[J].J Clin Ped Sur,2018,17(11):805-808.DOI:10.3969/j.issn.1671-6353.2018.11.002.
10 彭琨,周崇高,李碧香,等.加速康复外科理念在胆道闭锁围手术期的应用研究[J].临床小儿外科杂志,2019,18(12):1043-1048.DOI:10.3969/j.issn.1671-6353.2019.12.011.Peng K,Zhou CG,Li BX,et al.Application of enhanced recovery after surgery in perioperative management of biliary atresia[J].J Clin Ped Sur,2019,18(12):1043-1048.DOI:10.3969/j.issn.1671-6353.2019.12.011.
11 Ng VL,Haber BH,Magee JC,et al.Medical status of 219 children with biliary atresia surviving long-term with their native livers:results from a North American multicenter consortium[J].J Pediatr,2014,165(3):539-546.e2.DOI:10.1016/j.jpeds.2014.05.038.
12 Nio M,Wada M,Sasaki H,et al.Risk factors affecting late-presenting liver failure in adult patients with biliary atresia[J].J Pediatr Surg,2012,47(12):2179-2183.DOI:10.1016/j.jpedsurg.2012.09.003.
13 程卫,陈小爱,冯杰雄.营养风险筛查工具在胆道闭锁患者中的应用[J].临床小儿外科杂志,2015,14(1):68-70.DOI:10.3969/j.issn.1671-6353.2015.01.020.Cheng W,Chen XA,Feng JX.Application of a screening tool of nutrition risks for biliary atresia patients[J].J Clin Ped Sur,2015,14(1):68-70.DOI:10.3969/j.issn.1671-6353.2015.01.020.
14 Wong KKY,Wong CWY.A review of long-term outcome and quality of life of patients after Kasai operation surviving with native livers[J].Pediatr Surg Int,2017,33(12):1283-1287.DOI:10.1007/s00383-017-4158-4.
15 Chardot C,Buet C,Serinet MO,et al.Improving outcomes of biliary atresia:French national series 1986-2009[J].J Hepatol,2013,58(6):1209-1217.DOI:10.1016/j.jhep.2013.01.040.
16 Shimaoka S,Ohi R,Saeki M,et al.Problems during and after pregnancy of former biliary atresia patients treated successfully by the Kasai procedure[J].J Pediatr Surg,2001,36(2):349-351.DOI:10.1053/jpsu.2001.20713.
Memo
收稿日期:2020-04-26。
基金项目:国家自然科学基金(编号:81873545)
作者简介:郑珊,Email:szheng@shmu.edu.cn