Liu Jinqiao,Chen Wenjuan,Hu Yuan,et al.Diagnostic value of Berry syndrome by color Doppler echocardiography[J].Journal of Clinical Pediatric Surgery,,19():353-357.[doi:10.3969/j.issn.1671-6353.2020.04.014]
Diagnostic value of Berry syndrome by color Doppler echocardiography
- Keywords:
- Ultrasongraphy; Doppler; Color; Echocardiography; Berry syndrome; CT Vascular Reconstruction
- CLC:
- R54;R540.4+5
- Abstract:
- Objective To explore the value of color echocardiography in the diagnosis of Berry syndrome.Methods Eight children with Berry syndrome were diagnosed by color Doppler echocardiography from April 2010 to November 2019.PHILIPS IE33 and PHILIPS EPIQ 7C color Doppler echocardiography diagnostic instruments with S5-1,S8-3,X7-2 probes at a frequency of 2.5-7.5MHz were operated for conventional scans and short-axis view of aorta,long-axis view of pulmonary artery in right ventricular outflow tract,long-axis view of aortic arch of sternum and lower section of xiphoid.Main trunk shape and origin of left and right pulmonary artery branches,top branch structure of aortic arch and continuity of distal and descending aorta were observed.Results Eight patients with confirmed Berry syndrome underwent color Doppler echocardiography.Seven of them were diagnosed as Berry syndrome.One patient with preoperative echocardiography was diagnosed only with open ductus and narrowed aortic arch.After Berry syndrome was confirmed by CT vascular reconstruction,surgery was performed.Cardiac malformations included type Ⅱ aorta-pulmonary septal defect (n=8),right aortic abnormal origin aorta (n=8),aortic arch rupture (n=7),aortic arch stenosis (n=1) and open artery duct (n=8).Ventricular septum was continuous and intact and there were pulmonary hypertension and mild-to-moderate regurgitation of tricuspid valve; 7 cases with oval foramen were not closed.Seven children were cured by surgery.One child with severe pulmonary hypertension and severe pneumonia died preoperatively. Conclusion As a non-invasive examination modality,color echocardiography can more intuitively depict various malformations of Berry syndrome.A definite clinical diagnosis should be made in conjunctions with the findings of CT vascular reconstruction.
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Memo
收稿日期:2019-07-30。
基金项目:湖南省发改委基金（编号：湘发改投资[2014]658号）
通讯作者:周启昌,Email:hnzqc2013@163.com