Yang Yi,Yin Xiaoming.Gonadal management in 46,XY disorders of sexual development[J].Journal of Clinical Pediatric Surgery,,18():167-171.[doi:10.3969/j.issn.1671-6353.2019.03.002]
Gonadal management in 46,XY disorders of sexual development
- Keywords:
- Gonadal Dysgenesis; 46; XY/Embryo; Gender Identity
- CLC:
- R726.9;R691.1
- Abstract:
- Disorders of sex development (DSD) are a generic definition including any problem noted at birth where the genitalia are atypical in relation to chromosomes or gonads.According to the DSD classification of Chicago Conference,46,XY DSD is the most complex disorder of sexual development.Until now,optimal protocol has remained controversial in the gonad management of 46,XY DSD.Based upon a literature review and personal clinical experiences,gonadal management in 46,XY DSD was addressed from the aspects of gonadal biopsy and exploration,gonadal malignancy risks,follow-up strategies,timing and indication of gonadectomy.
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Memo
收稿日期:2018-11-27。
基金项目:国家自然基金面上项目（编号：81571514）
通讯作者:杨屹,Email:yangy2@sj-hospital.org