XU Min,GU Song,PAN Ci,et al.The management of non-wilms renal tumors in children[J].Journal of Clinical Pediatric Surgery,,12():93-96.[doi:10.3969/j.issn.1671— 6353.2013.02.005]
The management of non-wilms renal tumors in children
- Keywords:
- Kidney Neoplasms/TH; Child
- Abstract:
- Objetive To present our experience of managing non-wilms,renal tumors in children. Methods During From July 1998 to July 2010, 18 cases of non-wilms, renal tumors in children were treated.14 cases were male, 4 cases were female, age ranged from 9 years to 2 months, mean age was 40.17 ± 34.04 months.The pathological diagnosis included 9/18(50%)cases of clear cell sarcoma,2/18(11.1%)cases of rhabdoid tumor of kidney, 2/18(10.1%)cases of renal cell carcinoma,1/18(5.56%)case of mesoblastic nephroma, 1/18(5.56%)case of metanephric stromal tumor,1/18(5.56%)case of metanephric adenoma, 1/18(5.56%)cases of angiomyolipoma, 1/18(5.56%)case of primitive neuroectodermal tumor. Results 8/9cases of clear cell sarcoma cases were survival,whose average follow-up time was 24.56±17.27 months,1 case died after giving up treatment 1.5 year. 2/cases of rhabdoid tumor of kidney were survived after surgery and chemotherapy, follow-up time was 3 years and 4 years. 2 cases of renal cell carcinoma were survived after surgery, follow-up time was 13 months and 25 months. 1 case of primitive neuroectodermal tumor was survived after surgery and chemotherapy,follow-up time was 16 months. 1 case of mesoblastic nephroma、metanephric stromal tumor 、metanephric adenoma and angiomyolipoma survived without relapse. Conclusions Although non-wilms renal tumors is a small part of all kidney tumor, it is difficult to identify from other tumors. So pathological diagnosis is essential. Surgical treatment combined with radiotherapy and chemotherapy is essential.
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