Xu Wei,Yang Tianquan,Han Yong,et al.Diagnosis and treatment of dysembryoplastic neuroepithelial tumor[J].Journal of Clinical Pediatric Surgery,,22():383-386.[doi:10.3760/cma.j.cn101785-202101041-016]
Diagnosis and treatment of dysembryoplastic neuroepithelial tumor
- Abstract:
- Objective To explore the clinical characteristics and treatments of dysembryoplastic neuroepithelial tumor (DNET).Methods From December 2017 to May 2018,5 DNET children were reviewed.Etiologies,imaging features,classifications,treatments and prognoses were recorded.Results There were epileptic seizures(n=4) and headache,lethargy and other hydrocephalus symptoms(n=1).Computed tomography (CT) and magnetic resonance imaging (MRI) were performed.Based upon imaging characteristics,they were divided into type Ⅰ(n=1),type Ⅱ(n=3) and type Ⅲ(n=1).Type 1 underwent gyrus resection while type 3 resection of lesion in ventricle through ventriculoscopy.Type 2 underwent resection of temporal lobe lesion plus anterior medial temporal lobe(n=1) and subtotal resection of lesion due to an invasion of functional areas and basal ganglia(n=1).Conclusion Associated with imaging types,DNET is frequently manifested as epilepsy and hydrocephalus.Tumor resection alone or extended excision tumors and epileptogenic lobe often yield decent outcomes.
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Memo
收稿日期:2021-1-15。
基金项目:苏州市科技发展计划(民生科技)项目(SYSD2018116)
通讯作者:王勇强,Email:15151536919@163.com