Xia Bo,He Qiuming,Li Jiahua,et al.Early diagnosis and clinical outcome analysis of type Ⅲ congenital esophageal atresia with tracheomalacia[J].Journal of Clinical Pediatric Surgery,,20():1116-1121.[doi:10.12260/lcxewkzz.2021.12.003]
Early diagnosis and clinical outcome analysis of type Ⅲ congenital esophageal atresia with tracheomalacia
- Keywords:
- Esophageal Atresia/CN; Esophageal Atresia/CO; Esophageal Atresia/DI; Tracheomalacia/DI; Treatment Outcome
- CLC:
- R571;R562.1
- Abstract:
- Objective To explore the early diagnosis and clinical outcome of type Ⅲ congenital esophageal atresia (CEA) with tracheomalacia (TM), and to provide clinical reference for CEA with TM.Methods In the retrospective study, the clinical data of 15 cases with type Ⅲ CEA from November 2019 to December 2020 in Guangzhou Women and Children’s Medical Center were collected, and preoperative and postoperative airway assessment results based on endoscopy were analyzed.Results A total of 31 CEA cases were treated in our hospital, 15 cases assessed by pre-endoscopy were enrolled in this study, including 12 males and 3 females.The median gestational age was 38.3 (34~40.6) weeks.Among them, 14 (93.3%) cases complicated by TM including 2 cases with mild TM, 10 cases with moderate TM, and 2 cases with severe TM.In 8 cases, TM was more pronounced than preoperative TM when reassessed 1 month after surgery, including 3 cases with moderate TM and 5 cases with severe TM.Among 15 cases, 7 cases (46.7%) were diagnosed stricture, and 5 cases (33.3%) with gastroesophageal reflux diagnosed by image inspection.4 cases (26.67%) showed no symptoms after surgery, 11 cases (73.33%) presented with respiratory symptoms, and 2 of them underwent acute life-threatening events and both were successfully rescued.Conclusion TM are frequently associated with CEA and represent an important etiology of high morbidity and mortality of CEA.Electronic bronchoscopy can be used for early diagnosis and evaluation of TM.Life-threatening events may occur in TM patients, and long-term respiratory tract follow-up is recommended in order to get timely rescue.
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Memo
收稿日期:2021-06-09。
基金项目:广东省自然科学基金面上项目（编号：2020A1515010296）
通讯作者:何秋明,Email:qiuminghe@foxmail.com