Chen Gong,Zhang Jie.Emphasis on pulmonary vascular complications in children with a long-term survival after hepatoportal jejunostomy for biliary atresia[J].Journal of Clinical Pediatric Surgery,,():706-710.[doi:10.3760/cma.j.cn101785-202406012-002]
Emphasis on pulmonary vascular complications in children with a long-term survival after hepatoportal jejunostomy for biliary atresia
- Keywords:
- Biliary Atresia; Surgical Procedures; Operative; Postoperative Complications; Hepatopulmonary Syndrome; Pulmonary Arterial Hypertension
- Abstract:
- In children with a long-term survival after hepato-jejunostomy for biliary atresia (BA),chronic liver cirrhosis leads to hepatopulmonary syndrome (HPS) and portopulmonary hypertension (PoPH),causing diverse respiratory and circulatory system symptoms.The incidence of such complications in BA children is higher than that of other chronic liver diseases.With a faster progression,it endangers life in some severe cases.HPS and PoPH may coexist in the same child.Improving the understanding of HPS/PoPH,making an early diagnosis,rational selection of medication and proper timing of liver transplantation require multidisciplinary collaborations.
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Memo
收稿日期:2024-6-6。
基金项目:上海市自然科学基金 (19ZR1406600)
通讯作者:陈功,Email:chengongzlp@hotmail.com