Lu Hang,Tang Jie,Tang Weibing.Research advances on operative timing and preoperative bowel management of classic Hirschsprung disease[J].Journal of Clinical Pediatric Surgery,,():395-400.[doi:10.3760/cma.j.cn101785-202403060-018]
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Research advances on operative timing and preoperative bowel management of classic Hirschsprung disease

Journal of Clinical Pediatric Surgery[ISSN:1671-6353/CN:43-1380/R] volume: Number: 2024 No.04 Page: 395-400 Column: 综述 Date of publication: 2024-04-01
Author(s):
Lu Hang;  Tang Jie;  Tang Weibing
Department of Neonatal Surgery, Affiliated Children’s Hospital, Nanjing Medical University, Nanjing 210008, China
Keywords:
Hirschsprung Disease; Surgical Procedures;  Operative; Perioperative Care; Enema Therapy; Bowel Mangement
DOI:
10.3760/cma.j.cn101785-202403060-018
Abstract:
As one of the most common defecation disorders in children,Hirschsprung disease (HSCR) is characterized by an absence of intestinal ganglion cells.Its major treatment is surgical removal of involved intestine.With rapid advancement of medical technology and evolving concepts of diagnosis and therapy in recent years,about 80-90% of patients may be diagnosed during neonatal period.However,timing of pull-through surgery after a definite diagnosis has remained controversial and it is often delayed after neonatal period.Time from diagnosis to pull-through surgery and standardized bowel management are required to relieve distal intestinal obstruction,maintain bowel movements,improve nutrition and prevent an onset of Hirschsprung disease-associated enterocolitis (HAEC).This review focused upon timing of HSCR pull-through surgery,proper preoperative intestinal management and selecting protocols.

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Memo

收稿日期:2023-04-17。
基金项目:国家自然科学基金项目(81801496)
通讯作者:唐维兵,Email:twbcn@njmu.edu.cn

Last Update: 1900-01-01