Yin Qiang,Peng Yuming,Ji Chunyi,et al.Type V Congenital intrahepatic portosystemic shunt-patent ductus venosus with pulmonary hypertension as the first symptom: one case report with a literature review[J].Journal of Clinical Pediatric Surgery,,21():283-287.[doi:10.3760/cma.j.cn101785-201911014-015]
Type V Congenital intrahepatic portosystemic shunt-patent ductus venosus with pulmonary hypertension as the first symptom: one case report with a literature review
- Keywords:
- Hypertension; Pulmonary; Congenital Intrahepatic Portosystemic Venous Shunts; Patent Ductus Venosus
- Abstract:
- Objective To explore the clinical manifestations and treatment strategies of congenital intrahepatic portosystemic venous shunt (CIPSVS) in children with a review of literature.Methods The clinical and postoperative follow-up data was retrospectively analyzed for a child with type V CIPSVS, namely, patent ductus venosus (PDV) with pulmonary hypertension as the first symptom, and the relevant literature was reviewed and analyzed.Results The patient had repeated respiratory tract infection and pulmonary hypertension, and underwent venous catheter ligation.No respiratory tract infection occurred in the 6-month postoperative follow-up, with pulmonary hypertension lower than before.Relevant literature reports were analyzed simultaneously and 41 cases were included.There were 4 cases treated with interventional surgery, 17 cases with open surgery, and 3 cases with endoscopic surgery, all seeing clinical symptoms relieved after surgery.But there were 17 cases that did not report the treatment plan.Conclusion CIPSVS is a clinically rare disease with its clinical manifestations highly diverse.In the cases of liver dysfunction and abnormal metabolism due to insufficient hepatic portal blood perfusion, and abnormal perfusion of cardiopulmonary system, CIPSVS may be the possible cause.Its treatment require individualization.
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Memo
收稿日期:2019-11-07。
基金项目:湖南省卫生健康委课题（C2019011）
通讯作者:尹强,Email:qiangyin@hotmail.com