Sun Rui,Li Long.Research advances of surgery for cavernous transformation of portal vein in children[J].Journal of Clinical Pediatric Surgery,,19():1145-1151.[doi:10.3969/j.issn.1671-6353.2020.12.016]
Research advances of surgery for cavernous transformation of portal vein in children
- Keywords:
- Fortal Vein/AH; Hypertension; Portal; Fortal Pressure; Surgical Procedures; Operative; Child
- CLC:
- R575.2+1;R657.3+4
- Abstract:
- Cavernous transformation of the portal vein (CTPV) is a major cause of prehepatic portal hypertension in children.It may cause a series of portal hypertension syndromes such as hematemesis and melena.It not only affects children’s growth and development,but also endangers their lives in severe cases.Thus early diagnosis and treatment are recommended.At present,surgery is a major treatment for CTPV.The operative approaches include disconnection,shunting,superior mesenteric vein-left portal vein bypass (Rex operation) and operation plus liver transplantation,et al.Rex shunt is curative for CTPV due to its conformity with the physiological shunt of children.We conducted to review the latest domestic and international researches and related outcomes of various surgical approaches.And Rex operation is highlighted.This review is expected to provide a systematic understanding and reasonable selection of surgical approaches for pediatric CTPV.
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Memo
收稿日期:2019-09-10。
基金项目:北京市医院管理局儿科学科协同发展中心儿科专项重点项目（编号：XTZD20180302）；北京协和医学院2019年"中央高校基本科研业务费"立项项目（编号：3332019166）
通讯作者:李龙,Email:Lilong23@126.com