Li Xiaobing,Zhang Rufang,Shen Li,et al.Diagnosis and treatment of pleuropulmonary blastoma in children[J].Journal of Clinical Pediatric Surgery,,19():166-170.[doi:10.3969/j.issn.1671-6353.2020.02.015]
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Diagnosis and treatment of pleuropulmonary blastoma in children

Journal of Clinical Pediatric Surgery[ISSN:1671-6353/CN:43-1380/R] volume: 第19卷 Number: 2020 02 Page: 166-170 Column: 论著 Date of publication: 2020-02-20
Author(s):
Li Xiaobing;  Zhang Rufang;  Shen Li;  Gongjin;  Xie Yewei
Department of Cardiothoracic Surgery, Affiliated Shanghai Children’s Hospital, Shanghai Jiao Tong University, Shanghai 200062, China
Keywords:
Pleuropulmonary Blastoma/DI; Pleuropulmonary Blastoma/SU; Cystic Adenomatoid Malformation of Lung; Congenital/DI; Cystic Adenomatoid Malformation of Lung; Congenital/SU
CLC:
R734.1;R734.3;R734.2
DOI:
10.3969/j.issn.1671-6353.2020.02.015
Abstract:
Objective To explore the clinical characteristics,diagnosis and treatment of pleuropulmonary blastoma in children.Methods The clinical data were retrospectively analyzed for 6 hospitalized children with pleuropulmonary blastoma from October 2013 to June 2017.There were 3 boys and 3 girls with an age range of 14-120 months.There were partial lobectomy (n=1) and lobectomy (n=4).The follow-up period was 1 to 34 months.Results Five of them were initially misdiagnosed.The preliminary diagnosis was pneumonia (n=3),pleural effusion (n=1) and congenital cystic adenomatoid malformation (n=1).The follow-up outcomes were clinical recovery (n=1),survived with tumor & currently on regular chemotherapy (n=1) and death within 1 month post-operation (n=3).One patient relapsed after 1 month,was re-operated and died on the surgical day.Another child died within 2 month post-operation.Conclusion Due to non-specific clinical manifestations,pediatric pleuropulmonary blastoma is often misdiagnosed as congenital cystic adenomatoid malformation.Its postoperative prognosis is relatively decent.The treatment mainstays are an early discovery,an early operation and subsequent formal chemotherapy.

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Memo

收稿日期:2018-06-25。
通讯作者:张儒舫,Email:zhangrf@shchildren.com.cn

Last Update: 1900-01-01