BAI Song,LI Xiao feng,YUAN Feng,et al.Unifocalization repair for pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries.[J].Journal of Clinical Pediatric Surgery,,9():410.
Click Copy

Unifocalization repair for pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries.

Journal of Clinical Pediatric Surgery[ISSN:1671-6353/CN:43-1380/R] volume: 第9卷 Number: 2010 06 Page: 410 Column: Date of publication: 2010-12-28
Author(s):
BAI Song;  LI Xiaofeng;  YUAN Feng
et al.Heart Center of Beijing Children’s Hospital Affiliated to Capital University of Medical Sciences, Beijing 100045, China.
Keywords:
Heart Diseases/SU; Heart Defects; Congenital; Heart Septal Defects; Ventricular; Pulmonary Artery
Document code:
A
Abstract:
ObjectiveTo review the opertion experience and outcome of unifocalization repairs for PA with VSD and MAPCAs.MethodsFrom Jul. 2008 to Aug. 2010, 8 patients (male 3, female 5) with age ranged from 5 to 72 (median 8.2) months and body weight ranged from 4.5 to 13 (mean 8.7±2.8) kg were treated with unifocalization repairs. One case underwent radical operation. The other 7 cases underwent a multistaged repair approach.ResultsThere were no deaths, all cases were being referred to the outpatient department for followup which lasted for 6 to 20 months, When reasonable pulmonary vascularization has been obtained, there were 3 cases were treated with complete repair with transventricular closure of the VSD and right ventricular outflow tract reconstruction.ConclusionsUnifocalization as a palliative operation is a useful method for patients PA with VSD and MAPCAs. Staged repair yields a relatively low mortality rate with good functional results.

References:

1Ben DM,Shafi M.Unifocalization of major aortopulmonary collateral arteries in pulmonary atresia with ventricular septal defect is essential to achieve excellent outcomes irrespective of native pulmonary artery morphology\[J\].Thorac Cardiovasc Surg, 2009, 138: 1269—1275.
2Haworth SG.Collateral arteries in pulmonary atresia with ventricular septal defect: a precarious blood supply\[J\].Br Heart J, 1980,44:5—13.
3Gary K.OneStage Repair and Unifocalization for Pulmonary Atresia with Ventricular Septal Defect and Major Aortopulmonary Collateral Arteries in Early Infancy.
4Gary K. An overview of pulmonary atresia, ventricular septal defect, and multiple aorta pulmonary collateral arteries\[J\]. Pediatric Cardiology, 2009, 26: 65—70.
5Sunil P,Frank L.Surgical Management of Pulmonary Atresia With Ventricular Septal Defect and Major Aortopulmonary Collaterals: A ProtocolBased Approach\[J\].Pediatr Cardic Surg Ann, 2009, 12:145—151.
6SukWon Song,Han Ki Park.PA With VSD and MAPCA: 18Year Clinical Experience and Angiographic Followup of Major Aortopulmonary Collateral Arteries\[J\].Circ J, 2009, 73: 516—522.
7Richard A，Jonas.Comprehensive Surgical Management of Congenital Heart Disease\[M\].First published, Oxford University Press Inc，2004, 440—456.
8Nobuyuki Ishibashi,Toshiharu Shin,et al.Clinical results of staged repair with complete unifocalization for pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries\[J\].Cardiothoracic Surgery,2007, 32: 202—208.
9Ishibashi N,Shin’oka T.Clinical results of staged repair with complete unifocalization for pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries\[J\].Eur J Cardiothorac Surg,2007,32: 202—208.

Memo

Email:will_bs@yahoo.com

Last Update: 2010-12-01