Huang Wenya,Xiao Tian,Li Chunwang,et al.Interventional treatment for KasabachMerrit syndrome in children:a report of 7 cases.[J].Journal of Clinical Pediatric Surgery,2018,17(01):43-46.
血管瘤并血小板减少综合征介入栓塞治疗的效果分析
- Title:
- Interventional treatment for KasabachMerrit syndrome in children:a report of 7 cases.
- Keywords:
- Hemangioma; Thrombocytopenia; Syndrome; Interventional Treatment
- 文献标志码:
- A
- 摘要:
-
目的 分析血管瘤并血小板减少综合征经介入栓塞治疗的效果。 方法 收集２０１１年
１２月至２０１５年１２月间本院收治的７例ＫＭ综合征患儿作为研究对象，所用病例在ＤＳＡ透视下进行选
择性动脉栓塞治疗。 结果 ７例患者中，颌面部１例，躯干３例，肩部２例，颈部１例。血小板均在６０
×１０９／Ｌ以下，最少７×１０９／Ｌ。治愈４例，好转３例，无死亡病例，介入治疗效果良好。 结论 血管瘤
并血小板减少综合征患儿如果能早期选择介入治疗，多数病例预后较好，但无法根除原发灶的广泛性
血管畸形。介入手术治疗对颌面部、颈部、躯干部位的ＫＭ综合征疗效确切，副反应小，值得推广。
- Abstract:
- ObjectiveTo evaluate the clinical outcomes of KasabachMerrit syndrome and examine its interventional treatments.MethodsThis retrospective study was conducted for 7 patients with KasabachMerrit syndrome receiving selective arterial embolization by DSA (digital subtraction angiography).ResultsThe sites included maxillofacial region (n=1),trunk (n=3),shoulder (n=2) and neck (n=1).The count of platelet7×109/L to 60×109/L.The outcomes were cure (n=4) and improvement (n=3).ConclusionAt an early stage,this disease may be treated interventionally with an excellent prognosis.However,generalized primary vascular malformations are not eradicated in most cases.The prognosis is poor for combined platelet reduction.Interventional surgery of jawface,neck and trunk area of KM syndrome is effective and have few side effects.It is worthy of wider promotion.
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