Ma Zhihua,Tang Jie,Li Hongxing,et al.Modification and application progress of Swenson and Soave procedures for Hirschsprung’s Disease[J].Journal of Clinical Pediatric Surgery,2026,(05):436-440.[doi:10.3760/cma.j.cn101785-202510018]
Swenson与Soave术式治疗先天性巨结肠的术式改良及应用进展
- Title:
- Modification and application progress of Swenson and Soave procedures for Hirschsprung’s Disease
- Keywords:
- Hirschsprung’s Disease; Surgical Procedures; Operative; Child; Decision-Making
- 摘要:
- 先天性巨结肠(Hirschsprung’s disease,HSCR)是一种以肠道远端神经节细胞缺失为特征的先天性肠神经发育障碍性疾病,主要表现为肠道功能障碍。该病多见于新生儿或婴幼儿,临床症状以排便困难、喂养不良、体重增长不良及进行性腹胀为主。目前外科手术仍是主要治疗手段,术式核心目标为切除病变肠段并恢复肠道连续性。本文聚焦Swenson与Soave术式在HSCR治疗中的临床应用,回顾近年相关文献,综述两种术式的历史演变、技术改良及临床疗效,并探讨腹腔镜、机器人等微创技术与两种术式的融合应用及发展现状。
- Abstract:
- Hirschsprung’s disease (HSCR) is a congenital enteric neurodevelopmental disorder characterized by the absence of ganglion cells in the distal intestine,leading primarily to intestinal dysfunction.The disease most commonly affects neonates and infants,with clinical manifestations including difficulty in defecation,poor feeding,inadequate weight gain,and progressive abdominal distension.At present,surgical intervention remains the mainstay of treatment,with the core objective being the resection of the diseased bowel segment and restoration of intestinal continuity.This article focuses on the clinical application of the Swenson and Soave procedures in the treatment of HSCR.By reviewing recent literature,it summarizes the historical evolution,technical modifications,and clinical outcomes of these two procedures.In addition,it discusses the integration and current development of minimally invasive techniques,such as laparoscopy and robotic surgery,in combination with these procedures.
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备注/Memo
收稿日期:2025-10-14。
基金项目:江苏省卫生健康发展研究中心开放课题(JSHD2022027)
通讯作者:唐维兵,Email:twbcn@163.com