[1]郑园园,张澜,肖蜜黎,等.新生儿超短肠综合征营养支持1例[J].临床小儿外科杂志,2026,(04):387-390.[doi:10.3760/cma.j.cn101785-202502033]
　Zheng Yuanyuan,Zhang Lan,Xiao Mili,et al.Nutritional therapy for ultra-short bowel syndrome in neonates: one case report[J].Journal of Clinical Pediatric Surgery,2026,(04):387-390.[doi:10.3760/cma.j.cn101785-202502033]
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新生儿超短肠综合征营养支持1例

《临床小儿外科杂志》[ISSN:1671-6353/CN:43-1380/R] 卷: 期数: 2026年04 页码: 387-390 栏目: 小儿外科临床营养 出版日期: 2026-04-28
Title:
Nutritional therapy for ultra-short bowel syndrome in neonates: one case report
作者:
郑园园1;  张澜2;  肖蜜黎2;  董瑞3;  姚伟3;  杨童玲4;  唐子斐5;  王瑾2;  张蓉2;  郑珊3;  沈淳6;  钱甜1
1. 复旦大学附属儿科医院临床营养科, 上海 201100;
2. 复旦大学附属儿科医院新生儿科, 上海 201100;
3. 复旦大学附属儿科医院普外科, 上海 201100;
4. 复旦大学附属儿科医院护理部, 上海 201100;
5. 复旦大学附属儿科医院消化科, 上海 201100;
6. 复旦大学附属儿科医院新生儿外科, 上海 201100
Author(s):
Zheng Yuanyuan1;  Zhang Lan2;  Xiao Mili2;  Dong Rui3;  Yao Wei3;  Yang Tongling4;  Tang Zifei5;  Wang Jin2;  Zhang Rong2;  Zheng Shan3;  Shen Chun6;  Qian Tian1
1. Department of Clinical Nutrition, Affiliated Children’s Hospital of Fudan University, Shanghai 201100, China;
2. Department of Neonatology, Affiliated Children’s Hospital of Fudan University, Shanghai 201100, China;
3. Department of General Surgery, Affiliated Children’s Hospital of Fudan University, Shanghai 201100, China;
4. Department of Nursing, Affiliated Children’s Hospital of Fudan University, Shanghai 201100, China;
5. Department of Gastroenterology, Affiliated Children’s Hospital of Fudan University, Shanghai 201100, China;
6. Department of Neonatal Surgery, Affiliated Children’s Hospital of Fudan University, Shanghai 201100, China
关键词:
短肠综合征; 小肠结肠炎;  坏死性; 婴儿;  新生; 营养支持; 胃造口术; 肠道营养; 胃肠外营养
Keywords:
Short Bowel Syndrome; Enterocolitis; Necrotizing; Infant; Newborn; Nutritional Support; Gastrostomy; Enteral Nutrition; Parenteral Nutrition
DOI:
10.3760/cma.j.cn101785-202502033
摘要:
短肠综合征(short bowel syndrome,SBS)是导致儿童肠衰竭的主要原因,营养管理是决定预后的核心环节,其目标是改善肠道功能,促进肠适应。剩余小肠长度＜25 cm 或低于预期年龄长度10%的SBS称为超短肠综合征,其营养支持更具挑战性。本文报道1例坏死性小肠结肠炎(necrotizing enterocolitis,NEC)手术后发生超短肠综合征患儿的诊疗经过及营养支持经验。患儿为足月新生儿,术后小肠仅剩20 cm,无回盲瓣,通过术后尽早开始肠内营养、胃造口喂养联合周期性胃肠外营养、遵从低草酸原则合理添加辅食等多种营养支持策略,最终实现完全经口喂养和良好的生存质量。本病例提示,超短肠综合征患儿的成功救治需要依据指南给予个体化的营养支持治疗方案。
Abstract:
Short bowel syndrome (SBS) is a major cause of intestinal failure in children.And nutritional management has been a core prognostic factor.The goal of treatment is to improve intestinal function and promote intestinal adaptation.SBS with a remaining small intestine length of <25 cm or <10% of expected length for age is termed as ultra-short bowel syndrome.Nutritional support for this condition is more challenging.This review focused upon the diagnosis,treatment and nutritional support experience of a full-term child with ultra-short bowel syndrome due to necrotizing enterocolitis (NEC).Postoperatively,merely 20 cm of small intestine remained without an ileocecal valve.Through various nutritional support strategies,including early initiation of enteral nutrition,gastrostomy feeding,cyclical parenteral nutrition,reasonable addition of complementary foods on a low-oxalate principle,full oral feeding and excellent quality-of-life were ultimately achieved.Thus successful treatment of children with ultra-short bowel syndrome requires a personalized nutritional support protocol based upon guidelines.

参考文献/References:

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备注/Memo

收稿日期:2025-2-18。
通讯作者:钱甜,Email:drqiantian@fudan.edu.cn;沈淳,Email:chunshen@fudan.edu.cn

更新日期/Last Update: 1900-01-01