Xu Hongyan,Yang Wenping,Huang Hui,et al.Intestinal malakoplakia in children:one case report[J].Journal of Clinical Pediatric Surgery,2025,(11):1087-1089.[doi:10.3760/cma.j.cn101785-202411060-018]
儿童肠道软斑病1例
- Title:
- Intestinal malakoplakia in children:one case report
- 摘要:
- 软斑病(malakoplakia,MP)是一种罕见的组织细胞增生性病变,好发于泌尿生殖系统,多见于有免疫缺陷或免疫低下的成人,儿童病例极为罕见。本文报告1例肠道软斑病患儿的诊治过程,并应用免疫组化,特殊染色及基因测序进行分析,发现患儿有X-连锁无丙种球蛋白血症(B细胞缺陷病),镜下组织细胞胞质及间质中找到同心圆状、靶环样的软斑小体(Michaelis-Gutmann body,M-G小体),为后续患儿的治疗提供了有价值的参考依据。
相似文献/References:
[1]许芝林,王强,李琰,等.乙状结肠冗长症的术式选择探讨[J].临床小儿外科杂志,2010,9(06):432.
XU Zhi lin,WANG Qiang,LI Yan,et al.Initiatory exploration of the standard of surgical treatment methods for Dolichosigmoid.[J].Journal of Clinical Pediatric Surgery,2010,9(11):432.
[2]黄圣余 曾玉英 张清姬 林福贞 吴善苏 阮海燕 林秀银 陈勇斌. 经肛门结肠灌洗一期治疗小儿肠套叠左半结肠坏死的体会[J].临床小儿外科杂志,2011,10(06):474.
[J].Journal of Clinical Pediatric Surgery,2011,10(11):474.
[3]刘永东 胡强 李俊峰. 14例小儿乙状结肠冗长症手术治疗分析[J].临床小儿外科杂志,2015,14(04):345.
[4]王建峰,朱慧,陈杰.肠道间质细胞参与调控结肠动力的研究进展[J].临床小儿外科杂志,2022,21(12):1191.[doi:10.3760/cma.j.cn101785-202010023-017]
Wang Jianfeng,Zhu Hui,Chen Jie.Recent advances in gastrointestinal interstitial cells regulating colonic motility[J].Journal of Clinical Pediatric Surgery,2022,21(11):1191.[doi:10.3760/cma.j.cn101785-202010023-017]
[5]李春芳,袁佳雨,李亚洲,等.儿童腹膜后脓肿并发结肠腹膜外穿孔1例[J].临床小儿外科杂志,2024,23(04):393.[doi:10.3760/cma.j.cn101785-202403060-017]
Li Chunfang,Yuan Jiayu,Li Yazhou,et al.Retroperitoneal abscess complicated by extraperitoneal colonic perforation in children:one case report[J].Journal of Clinical Pediatric Surgery,2024,23(11):393.[doi:10.3760/cma.j.cn101785-202403060-017]
[6]陶天,张晓威,赵扬,等.机器人辅助腹腔镜结肠Yang-Monti-Huixia术修复输尿管长段狭窄的初步应用[J].临床小儿外科杂志,2025,(06):548.[doi:10.3760/cma.j.cn101785-202503117-008]
Tao Tian,Zhang Xiaowei,Zhao Yang,et al.Preliminary application of robotic-assisted laparoscopic colon Yang-Monti-Huixia procedure for the repair of long-segment Ureteral Strictures[J].Journal of Clinical Pediatric Surgery,2025,(11):548.[doi:10.3760/cma.j.cn101785-202503117-008]
备注/Memo
收稿日期:2024-11-28。
基金项目:江西省卫生健康委科技计划项目[202510570]
通讯作者:徐红艳,Email:xhy_1983@126.com