Zheng Shan.Several outstanding issues in long-term survival of children with biliary atresia[J].Journal of Clinical Pediatric Surgery,2020,19(06):469-472.[doi:10.3969/j.issn.1671-6353.2020.06.001]
胆道闭锁患儿获得长期生存需要关注的问题
- Title:
- Several outstanding issues in long-term survival of children with biliary atresia
- Keywords:
- Biliary Atresia; Therapy; Quality of Life; Child
- 分类号:
- R722;R575.7;R725.7
- 摘要:
- 中国大陆胆道闭锁患儿的诊断和治疗水平已得到明显提高，而自体肝长期生存率及生存质量还需要进一步提高。对葛西手术后并发症及肝纤维化的长期规范随访，多学科合作的综合诊治，生长发育的长期监测，合理的营养及预防接种指导，以及肝移植的最佳时机选择，是帮助胆道闭锁患儿获得高质量长期生存的重要因素。
- Abstract:
- The diagnosis and treatment of children with biliary atresia (BA) in China mainland have significantly improved.However,long-term native liver survival rate and quality of life should be further optimized.Long-term standard follow-ups of Kasai postoperative complications and liver fibrosis,comprehensive treatments with multidisciplinary cooperations,long-term monitoring of growth and development,reasonable nutrition and vaccination guidance and appropriate timing for liver transplantation are the critical factors to help BA children to obtain long-term high-quality survival.
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备注/Memo
收稿日期:2020-04-26。
基金项目:国家自然科学基金（编号：81873545）
作者简介:郑珊,Email:szheng@shmu.edu.cn