Yuan Qiang,Yan Xueqiang.Recent advances of clinical trials of congenital prepubic sinus[J].Journal of Clinical Pediatric Surgery,2021,20(05):478-481.[doi:10.12260/lcxewkzz.2021.05.016]
先天性耻骨前窦道的临床研究进展
- Title:
- Recent advances of clinical trials of congenital prepubic sinus
- 关键词:
- 先天性耻骨前窦道/病因; 先天性耻骨前窦道/诊断; 先天性耻骨前窦道/外科学; 手术后并发症
- Keywords:
- Congenital Prepubic Sinus/ET; Congenital Prepubic Sinus/DI; Congenital Prepubic Sinus/SU; Postoperative Complications
- 分类号:
- R681.6;R726.8
- 摘要:
- 先天性耻骨前窦道是一种罕见的先天性畸形，其病因及胚胎学理论尚不明确。可能的病因包括腹壁闭合异常、变异的尿道背侧重复、尿生殖窦的先天性瘘管、泄殖腔的持续残留、泄殖腔膜残留和脐阴沟。先天性耻骨前窦道患者临床症状通常不明显，主要表现为窦道开口处透明黏液样分泌物渗出。超声、窦道造影及MRI检查有助于明确诊断及术前评估。手术切除有效，早期干预很有必要，可以避免反复发作感染等并发症。
- Abstract:
- As an extremely rare congenital malformation,congenital prepubic sinus has elusive etiological and embryological origins.Its potential causes include abnormal abdominal wall closure,variant of dorsal urethral duplication,congenital fistula of primitive urogenital sinus,persistent cloacal residue,residual cloacal membrane and umbilicophallic groove.The clinical symptoms are frequently not overt.And a major manifestation is an exudation of transparent mucus-like secretion at sinus opening.Ultrasound,fistulography and magnetic resonance imaging (MRI) may confirm a diagnosis and contribute to preoperative evaluations.Surgical resection is effective and early intervention necessary for preventing recurrent infections and other complications.
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备注/Memo
收稿日期:2020-08-13。
通讯作者:闫学强,Email:yangxueqiang@163.com