Tang Daxing.The occurrence of initial process of 46,XY sex abnormal development and the corresponding management suggestions[J].Journal of Clinical Pediatric Surgery,2019,18(03):161-166.[doi:10.3969/j.issn.1671-6353.2019.03.001]
46,XY性别发育基本过程相关异常的发生及处理建议
- Title:
- The occurrence of initial process of 46,XY sex abnormal development and the corresponding management suggestions
- Keywords:
- Gonadal Dysgenesis; 46; XY/Embryo; Sexual Development/Genetics
- 分类号:
- R726.9;R691.1
- 摘要:
- 本文根据近年来相关性别发育的文献报道，对目前已了解的胚胎时期46，XY性别发育基本过程进行了回顾，同时对其中几个重要节点出现异常进而产生相应临床症状进行了分析阐述，并提出相应处理意见。此外，针对小儿外科临床常见手术过程中易出现的几种意外的涉及性别发育异常的情况分别进行了描述，并给出了相应的处理建议。
- Abstract:
- Based on the relevant literature reports in recent years,this paper reviews the basic process of 46,XY sex development in embryonic period,and analyzes and expounds the abnormal clinical symptoms of several important key points,and puts forward some corresponding treatment opinions.In addition,several unexpected issues involving sex abnormal development were described in the course of common surgical procedures in pediatric surgery and the corresponding suggestions for management were given.
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备注/Memo
收稿日期:2018-11-26。
基金项目:国家重点研发计划—开展出生缺陷综合防治技术的应用示范和评价研究（编号：2018YFC1002700）
作者简介:唐达星,Email:tangdx0206@zju.edu.cn