小儿法乐四联症围术期的治疗策略

《临床小儿外科杂志》[ISSN:1671-6353/CN:43-1380/R] 卷: 第11卷期数: 2012年01期页码: 13-15 栏目: 论著出版日期: 2012-02-28

作者:: 周智恩冯君熊霞霞孙小圣陈红英杜娟王道庄邓硕曾; 成都心血管病医院心外科

关键词:: ; 法乐四联症; 外科学; 儿童

文献标志码:: A

摘要:: 目的总结法乐四联症（TOF）患儿手术治疗经验，探讨手术时机、手术适应证和围术期处理。方法回顾性分析我科2004年1月至2010年6月收治的132例小儿TOF的临床资料，其中男98例，女34例；年龄4个月至12岁，平均12.85岁。术前均行超声心动图或心导管造影检查确诊，均在体外循环下行根治性手术，部分病例以自体心包或带瓣自体心包扩大右室流出道和（或）肺动脉，对合并畸形作相应处理。结果本组围术期死亡4例（3.03%），其中2例死于术后多器官功能衰竭，2例死于低心排出量综合征。随访129例，随访时间12~90个月；失访3例。6例残余微量分流，生长发育正常，无不适。结论对症状显著的TOF患儿应尽早手术矫治，提高手术水平，加强术后监护是确保手术成功的关键。

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